Syndrome de Gougerot-Sjögren et maladie de Waldenström avec atteinte pulmonaire et hypercalcémieGougerot-Sjögren’s syndrome and Waldenström disease. La pathogénie des LMNH au cours du syndrome de Gougerot-Sjögren se fait en thérapeutique en fonction de l’extension et de l’évolution de la maladie. Le syndrome de Sjögren (SS) est une maladie immunitaire caractérisée par une dégénérescence progressive des glandes exocrines, aboutissant à un.

Author: Faerr Tygoshura
Country: Hungary
Language: English (Spanish)
Genre: History
Published (Last): 14 July 2014
Pages: 329
PDF File Size: 4.16 Mb
ePub File Size: 16.55 Mb
ISBN: 449-5-47788-304-4
Downloads: 21383
Price: Free* [*Free Regsitration Required]
Uploader: Kajira

Retrieved 15 July Environmental factors, such as glandular viral infectioncould prompt epithelial cells to activate the HLA-independent innate immune system through toll-like receptors. Seropositivity for anti-Ro and anti-La is associated with greater severity and longer duration of disease, and findings of their high abundance from the salivary glands of SS patients suggests their imperative role in the pathogenesis of SS.

Ann N Y Acad Sci.

Pan African Medical Journal

Systemic lupus erythematosus Subacute bacterial endocarditis Rheumatoid arthritis. The cause of SS is unknown, but it may be the influence of a combination of genetic, environmental, and other factors—as is the case with many other autoimmune disorders. Oral mucosa — Lining of mouth.

The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. Hypersensitivity and autoimmune diseases Microchimerism of fetal cells offspring lymphoid cells in maternal circulation may generate autoimmunity in women who have been previously pregnant.

Skin dryness in some people with SS may be the result of lymphocytic infiltration into skin glands. Some people may experience only the mild symptoms of dry eyes and mouth, while others have symptoms of severe disease. Moisture replacement therapies such as artificial tears may ease the symptoms of dry eyes.

Related Posts  ASP FT160AR PDF

Squamous cell papilloma Keratoacanthoma Malignant: Salivary glands Benign lymphoepithelial lesion Ectopic salivary gland tissue Frey’s syndrome HIV salivary gland disease Necrotizing sialometaplasia Mucocele Ranula Pneumoparotitis Salivary duct stricture Salivary gland aplasia Salivary gland atresia Salivary gland diverticulum Salivary gland fistula Salivary gland hyperplasia Salivary gland hypoplasia Salivary gland neoplasms Benign: SS is the second most common rheumatic autoimmune disorder, behind rheumatoid arthritis RA and systemic lupus erythematosus SLE.

A meta-analysis of worldwide studies”. Some research showed that the lack of vitamin A and vitamin D are associated with this disease.

Orphanet: Syndrome de Gougerot Sjogren

Environmental maldaie hormonal factors, in concert with an appropriate genetic background, are believed to trigger SS, which dysregulates epithelial cells and allows aberrant homing and activation of dendritic cells DCsT cells, and B cells. Retrieved from ” https: Atopic eczema Allergic urticaria Allergic rhinitis Hay fever Allergic asthma Anaphylaxis Food allergy common allergies include: Nine out of ten SS patients are women.

Middle age [2] [3]. Temporomandibular jointsmuscles of mastication maladiie malocclusions — Jaw joints, chewing muscles and bite abnormalities Bruxism Condylar resorption Mandibular dislocation Malocclusion Crossbite Open bite Overbite Overeruption Overjet Prognathia Retrognathia Scissor bite Maxillary hypoplasia Temporomandibular joint dysfunction.

Teeth pulpdentinenamel. In women with SS, vaginal dryness, vulvodynia and dyspareunia painful sexual intercourse are often reported; personal lubricants are recommended to help lessen irritation or pain that may result from dryness in the vaginal and vulva areas. An Orphanet summary for this disease is currently under development.

Archived from the original on 10 September Periodontium gingivaperiodontal ligamentcementumalveolus — Gums and tooth-supporting structures.

Maladie de Crohn associée à un syndrome de gougerot sjogren – EM|consulte

Other search option s Alphabetical list. Lymphomagenesis in primary SS patients is considered as a multistep process, with the first step being chronic stimulation of autoimmune B cells, especially B cells that produce rheumatoid factor at sites targeted by the disease. D ICD – Summary and related texts. The relationship of autoantibodies expressed in SS with apoptosis is still being researched.


Only comments written malaxie English can be processed. Although SS occurs in msladie age groups, the average age of onset is between ages 40 and 60, although experts note that up to half of all cases may be left undiagnosed or unreported. Adenosquamous carcinoma Basaloid squamous carcinoma Mucosal melanoma Spindle cell carcinoma Squamous cell carcinoma Verrucous carcinoma Oral florid papillomatosis Oral melanosis Smoker’s melanosis Pemphigoid Benign mucous membrane Pemphigus Plasmoacanthoma Stomatitis Aphthous Denture-related Herpetic Smokeless tobacco keratosis Submucous fibrosis Ulceration Riga—Fede disease Verruca vulgaris Verruciform xanthoma White sponge nevus.

There was a problem providing the content you requested

The hallmark symptom of SS is dry mouth and keratoconjunctivitis sicca dry eyes. Also, people who take drugs to suppress the immune system are more likely to develop cancer later.

Clinical Immunology and Immunopathology. Apart from this notably higher incidence of malignant NHL, SS patients show only modest or clinically insignificant deterioration in specific organ-related function, which explains the only slight increases in mortality rates of SS patients in comparison with the remainder of the population.